I am a
Home I AM A Search Login

Papers of the Week

2022 Sep 18

Allergy Asthma Clin Immunol



Systemic lupus erythematosus with various clinical manifestations in a patient with hereditary angioedema: a case report.


Ushio Y, Wakiya R, Kameda T, Nakashima S, Shimada H, Mansour M M F, Kato M, Miyagi T, Sugihara K, Mino R, Mizusaki M, Ibuki E, Kadowaki N, Dobashi H
Allergy Asthma Clin Immunol. 2022 Sep 18; 18(1):84.
PMID: 36117202.


Hereditary angioedema (HAE) is an inherited disease characterized by recurrent angioedema without urticaria or pruritus. The most common types of HAE are caused by deficiency or dysfunction in C1 esterase inhibitor (C1-INH-HAE). The association between C1-INH-HAE and systemic lupus erythematosus (SLE) is known; however, variations in the underlying pathophysiology, disease course, and treatment in this population remain incompletely understood.