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Papers of the Week

2022 Sep

Urol Case Rep


Pediatric cystectomy for refractory cystitis post-bone marrow transplant in dyskeratosis congenita: A case report.


Robinson E, Seideman C, Wong T, Hakar M, Austin CJ
Urol Case Rep. 2022 Sep; 44:102163.
PMID: 35873895.


We present a case of refractory cystitis after BK-virus associated hemorrhagic cystitis following bone marrow transplantation requiring cystectomy in a 17-year-old female with genetically confirmed dyskeratosis congenita, a telomere disorder characterized by early bone marrow failure. She presented with a contracted, small bladder with intense urinary symptoms non-responsive to conservative therapy and requiring opioids for pain control. Cystectomy is a rare, final surgical treatment for benign bladder conditions, especially among younger patients, and she experienced successful resolution of symptoms and cessation of chronic opioids post-intervention.