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Papers of the Week


2022 Feb 17


J Cosmet Dermatol

Lipoid Proteinosis: A Systematic Presentation of an Unusual Disease.

Authors

Mofarrah R, Ghasemi M, Mofarrah R, Emadi S, Rostamian F
J Cosmet Dermatol. 2022 Feb 17.
PMID: 35176194.

Abstract

Lipoid Proteinosis (LP) or Hyalinosis Cutis et Mucosae or Urbach-Wiethe disease is a rare autosomal recessive genodermatosis characterized by an amorphous hyaline material deposition in the skin mucosa and viscera. The clinical symptoms of this disease often begin in childhood, which persist throughout life. Skin manifestations include inflammation, scaling, acne, and eventually ulceration, and hyaline amorphous deposits in these areas of the wound cause a waxy and thick appearance on the skin. In addition, wounds leave atrophic scars like chickenpox.