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Papers of the Week

2022 Jan 13

Surg Case Rep



Clinical outcomes of surgical management for rare types of progressive familial intrahepatic cholestasis: a case series.


Masahata K, Ueno T, Bessho K, Kodama T, Tsukada R, Saka R, Tazuke Y, Miyagawa S, Okuyama H
Surg Case Rep. 2022 Jan 13; 8(1):10.
PMID: 35024979.


Progressive familial intrahepatic cholestasis (PFIC) is a heterogeneous group of genetic autosomal recessive diseases that cause severe cholestasis, which progresses to cirrhosis and liver failure, in infancy or early childhood. We herein report the clinical outcomes of surgical management in patients with four types of PFIC.