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Papers of the Week

2020 May 07

Eur J Ophthalmol

Rituximab in the treatment of Susac’s syndrome: Report of a case.


Monferrer-Adsuara C, Remolí-Sargues L, Hernández-Bel L, Gracia-García A, Hernández-Garfella M L, Cervera-Taulet E
Eur J Ophthalmol. 2020 May 07:1120672120924545.
PMID: 32380850.


Susac's syndrome is a rare retinocochleocerebral immune-mediated endotheliopathy and clinically manifests as a pathognomonic triad of encephalopathy, hearing loss, and branch retinal artery occlusion. This triad is rarely present at symptom onset, thus, it is often initially misdiagnosed. To date, Susac's syndrome has persisted as an elusive entity and there are numerous treatment regimens proposed with varying effectiveness mainly based on case series.