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Papers of the Week

2019 Oct 12

Endocrinol Diabetes Metab Case Rep


Pheochromocytoma arising from an ectopic adrenal tissue in multiple endocrine neoplasia type 2A.


Ohsugi H, Takizawa N, Kinoshita H, Matsuda T
Endocrinol Diabetes Metab Case Rep. 2019 Oct 12; 2019.
PMID: 31610522.


A 21-year-old woman was referred to our hospital to treat bilateral pheochromocytomas (PCCs) after a diagnosis of multiple endocrine neoplasia type 2A (MEN2A). We performed bilateral laparoscopic adrenalectomy. One year after the operation, urinary fractionated metanephrines in 24-h urine increased. MRI showed a 30 mm tumor on the interaortocaval region and 123I-MIBG concentrated in this area. We excised the tumor and performed para-aortic lymphadenectomy. Histopathologic examination confirmed a PCC arising from ectopic adrenal tissue. Urinary fractionated metanephrines in 24-h urine declined to basal levels immediately after the operation. We detected no recurrence of paraganglioma or PCC for 5 years after the treatment.